A Case of Ovarian Mature Cystic Teratoma in Woman with Turner syndrome.

Nam, Hyun Woo; Lee, Jin Hee; Kim, Yoon Sook; Kim, Jong Soo; Choi, Seung Do; Bae, Dong Han

Case Report

Korean Journal of Obstetrics & Gynecology 2005;48(4):1029-1032.
Published online April 1, 2005.

A Case of Ovarian Mature Cystic Teratoma in Woman with Turner syndrome.

Hyun Woo Nam, Jin Hee Lee, Yoon Sook Kim, Jong Soo Kim, Seung Do Choi, Dong Han Bae

Department of Obstetrics and Gynecology, College of Medicine, Soonchunhyang University, Soonchunhyang Chunan Hospital, Chunan, Korea. IM_Doc@hotmail.com

Abstract

Ovarian tumors in patients with Turner's syndrome are extremely rare. Turner syndrome occurs in 1 of 4000 to 10,000 live births, giving an approximate incidence of 1 to 2,500 live female births. Approximately half of the patients with Turner syndrome have "pure" 45,X cells in peripheral blood lymphocytes. Thirty to forty percents of Turner syndrome patients present mosaicism: 10-15% of the total group are 45,X/46,XX and 2 to 5% are 45,X/46,XY. In 45,X/46,XY Turner syndrome, the risk of developing a tumor is as high as 15-25%, with the possible development of dysgerminoma or gonadoblastoma. Recently, we experienced a case of a very rare left ovarian mature cystic teratoma in a 45,X/46,XX Turner syndrome, so report with a brief review of literature.

Key Words: Ovarian mature cystic teratoma, Turner syndrome