A Case of Type II Congenital Cystic Adenomatoid Malformation of the Lung in a Transdiaphragmatic Extralobar Pulmonary Sequestration.

Bae, Seong Keun; Kim, Ji Young

Case Report

Korean Journal of Obstetrics & Gynecology 2003;46(8):1604-1609.
Published online August 1, 2003.

A Case of Type II Congenital Cystic Adenomatoid Malformation of the Lung in a Transdiaphragmatic Extralobar Pulmonary Sequestration.

Seong Keun Bae, Ji Young Kim

¹Department of Obstetrics and Gynecology, College of Medicine, Pochon CHA University, Seoul, Korea.
²Department of Pathology, College of Medicine, Pochon CHA University, Seoul, Korea.

Abstract

With the current widespread use of obstetric ultrasonography, increasing cases of congenital malformations have been demonstrated antenatally. Both pulmonary sequestration and congenital cystic adenomatoid malformation of the lung (CCAM) are two infrequent congenital pulmonary diseases. The combination of these entities is rare. In the review of literature, this abnormality is so rare that only 80 cases were reported worldwide. To our knowledge, there has been no report that this combined malformation is located transdiaphragmatically. We report the first case of transdiaphragmatic extralobar pulmonary sequestration (ELS) associated with CCAM which was diagnosed by prenatal ultrasonography at 24 weeks gestational age.

Key Words: Extralobar pulmonary sequestration, Congenital cystic adenomatoid malformation