Two Cases of Mayer-Rokitansky-Kster-Hauser Syndrome Managed by McIndoe Operation.

Doh, Eun Hyung; Kang, Min A; Choi, Suck Chul; Yang, Hoei Saeng; Bae, Cheol Seong; Yoon, Hae Won; Sim, Jae Chul; Lee, Jong Moon

Case Report

Korean Journal of Obstetrics & Gynecology 1997;40(10):2350-2354.
Published online January 1, 2001.

Two Cases of Mayer-Rokitansky-Kster-Hauser Syndrome Managed by McIndoe Operation.

Eun Hyung Doh, Min A Kang, Suck Chul Choi, Hoei Saeng Yang, Cheol Seong Bae, Hae Won Yoon, Jae Chul Sim, Jong Moon Lee

Abstract

Mayer-Rokitansky-Kster-Hauser Syndrome is characterized by the absence of the vagina and uterus, the presence of apparently normal tubes and ovaries, feminine appeara-nce, normal female secondary sexual characteristics, a normal 46,XX karyotype, and a fem-inine psychosexual orientation. Various methods of surgical treatment have been introduced, but the ideal method is still not found. The two cases reviewed in this paper were all treated with McIndoe operation using full thickness skin graft. Both women were satisfied with vaginal depth and excellent result was achieved. We report two vaginoplasties in patients of Mayer-Rokitansky-Kster-Hauser Syndr- ome including a brief review of literature.