A case of aggressive angiomyxoma of the vulva. |
Byung Joon Park, Yong Wook Kim, Tae Eung Kim, Lee So Maeng |
1Department of Obstetrics and Gynecology, Incheon st. Mary's Hospital, College of Medicine, The Catholic University of Korea, Incheon, Korea. tekim@catholic.ac.kr 2Department of Pathology, Incheon st. Mary's Hospital, College of Medicine, The Catholic University of Korea, Incheon, Korea. |
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Abstract |
Aggressive angiomyxoma is an uncommon soft-tissue neoplasm which affects the pelvis and genital organs of the young female predominantly. This tumor has a high tendency of local recurrence, but it usually does not develop metastasis. Although surgical excision with wide tumor-free margins may be necessary to obtain a complete cure, some of patients experience local recurrences. Many of the tumors are estrogen receptor (ER) and progesterone receptor (PR) positive and medical therapy with gonadotropin-releasing hormone (GnRH) agonists showed to be effective in a few cases. We present a case of 29-years-old women who has aggressive angiomyxoma which was misdiagnosed as bartholin duct cyst. She was treated by wide local excision with postoperative adjuvant GnRH agonist therapy for 3 months. She is now free of disease during 9 months of follow up. We have described this case with the brief of literature. |
Key Words:
Aggressive angiomyxoma, Vulva |
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