A case of prune-belly syndrome in antenatal ultrasonography.

Jung, Kum Ji; Park, Ae Byul; Choi, Yoon Jung; Chun, Yea Young; Kang, Yong Pil; Sun, Jin Gyu; Kee, Kwang Soo

Case Report

Korean Journal of Obstetrics & Gynecology 2002;45(7):1250-1253.
Published online July 1, 2002.

A case of prune-belly syndrome in antenatal ultrasonography.

Kum Ji Jung, Ae Byul Park, Yoon Jung Choi, Yea Young Chun, Yong Pil Kang, Jin Gyu Sun, Kwang Soo Kee

Department of Obstetrics and Gynecology Kwangju Christian Hospital, Kwangju, Korea.

Abstract

Prune-belly syndrome is a rare compound fetal anomaly, characterized by absence or hypoplasia of abdominal wall musculature associated with urinary tract abnormalities and cryptorchidism. The prenatal ultrasound diagnosis was based on the findings of a lower abdominal cystic echo caused by abnormal dilatation of the bladder, upward compression of small intestines and decreased amniotic fluid volume. We experienced a case of Prune-belly syndrome diagnosed by ultrasound in a 12 weeks fetus following to IVF-ET pregnancy. Termination was performed at 12 weeks and autopsy confirmed the distended bladder, absence of abdominal muscles and urethra. So, we reported this case with a brief review of literature.

Key Words: Prune-belly syndrome, Antenatal diagnosis