A Case of Antenatally Diagnosed Cystic Adenomatoid Malformation of Lung.

Kang, S Y; Hwang, E S; Jeong, N J; Jae, M K

Case Report

Korean Journal of Obstetrics & Gynecology 1998;41(7):2001-2004.
Published online January 1, 2001.

A Case of Antenatally Diagnosed Cystic Adenomatoid Malformation of Lung.

Abstract

Congenital cystic adenomatoid malformation (CCAM) is a rare variant of congenital pulmonary cystic disease. It is characterized by cessation of bronchiolar maturation with an over-growth of mesenchymal elements and proliferation of polypoid glandular tissue in the absence of normal alveolar differentiation. Approximately, 200cases have been reported in the literature in the world and the antenatal diagnosis by ultrasonography has been described in several case reports. In 80% to 95% of cases, CCAM of the lung is confined to a single lobe and there is no lobe predilection for right and left predominance. The early diagnosis of the lethal macrocystic form of abnormality before a gestational age 25wks allowed the elective termination of pregnancy. We report one case of this condition where the diagnosis was made antenatally.

Key Words: Cystic adenomatoid malformation, Antenatal diagnosis