Congenital lobar emphysema with cystic lung abnormality: Antenatal ultrasound appearance.

Lee, Youn Jeong; Jeong, Hyun Chul; Joo, Heui Jin; Kim, Gwang Jun

doi:2012.55.11.834

Obstet Gynecol Sci > Volume 55(11); 2012 > Article

Case Report

Korean Journal of Obstetrics & Gynecology 2012;55(11):834-838.
Published online: November 16, 2012
DOI: https://doi.org/10.5468/KJOG.2012.55.11.834

Congenital lobar emphysema with cystic lung abnormality: Antenatal ultrasound appearance.

Youn Jeong Lee, Hyun Chul Jeong, Heui Jin Joo, Gwang Jun Kim

Department of Obstetrics and Gynecology, Chung-Ang University Hospital, Chung-Ang University College of Medicine, Seoul, Korea. gjkim@cau.ac.kr

Abstract

A 33-year-old woman at 23(+2) weeks of gestational age was referred for consultation due to the findings of a cyst in the right lung of the fetus. Prenatal ultrasound showed a 3 cm-sized hypoechogenic cyst, suggesting congenital cystic adenomatoid malformation. As the cyst grew and compressed the heart, serial cyst aspirations were performed. The cyst was proved to be congenital lobar emphysema on postnatal histopathologic exam. No other anomaly was found. Only few cases of congenital lobar emphysema (CLE) have been reported up to date and the prenatal diagnosis is extremely rare. Typically, fetal sonographic features of CLE have a bright echogenic lung and, to date, only 3 cases have been reported to have a cystic lesion. We report a case of a fetus with a cystic lung abnormality and postnatally proved congenital lobar emphysema.

Keywords: Congenital lobar emphysema; Prenatal diagnosis; Ultrasound; Lung