-
Case Report
-
Korean J Obstet Gynecol. 2009;52(3):377-381. Published online March 1, 2009.
- A case of peritoneal desmoplastic small round cell tumor.
-
Ki Yeol Yang, Young Sun Kim, Ji Hyun Han, Yong Ku Park, Min Hyung Jung
-
1Department of Obstetrics and Gynecology, Kyung Hee Medical Center, School of Medicine, Kyung Hee University, Seoul, Korea. webhospital@naver.com
2Department of Pathology, Kyung Hee Medical Center, School of Medicine, Kyung Hee University, Seoul, Korea.
- Abstract
- Desmoplastic small round cell tumor is a rare and aggressive tumor that affects young males. It is usually an abdominopelvic malignancy that demonstrates distinct histological appearances and a unique cytogenetic profile. There have been many different approaches to the treatment of desmoplastic small round cell tumor, but unfortunately it remains incurable and has poor long-term survival rates. However, with an aggressive approach to the treatment using multiple modalities, some temporary benefit to survival can be achieved. There has not yet been a case in which treatment has led to a curative outcome. Recently, we also experienced a case of very poor outcome of 31-year-old female with small round cell tumor in peritoneum. Here, we report the case with a brief review of literatures.
Keywords :Desmoplastic small round cell tumor;Peritoneum
