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Case Report
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Korean J Obstet Gynecol. 2003;46(1):184-187. Published online January 1, 2003.
- A case of McCune-Albright syndrome.
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Sun Young Jeong, Min Kyung Song, Jin Woo Lee
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Department of Obstetrics and Gynecology, College of Medicine, Catholic University, Seoul, Korea.
- Abstract
- McCune-Albright syndrome is a rare disease. It's triad is 1) precocious puberty, 2) fibrous dysplasia of bone and 3) caf-al-lait spots on skin. The cause is known as the mutation of subunit of G protein. Although there are some suggestions of treatment regimens including antiestrogen and GnRH agonist, at present, the accurate management is not known. We have experienced a case of McCune-Albright syndrome who has precocious puberty and fibrous dysplasia without caf-al-lait spot, and we present the case with a review of related literatures.
Keywords :McCune-Albright syndrome;precocious puberty;fibrous dysplasia;caf-al-lait spots;G-protein
