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Case Report
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Korean J Obstet Gynecol. 2003;46(1):166-170. Published online January 1, 2003.
- A case of complete testicular feminization syndrome with Inguinal Hernias.
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Hwa Young Choe, Sung Hong Joo, Ye Jin Kim, Sung Jin Cho
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Department of Obstetrics and Gynecology, National Medical Center, Seoul, Korea.
- Abstract
- Complete testicular feminization syndrome (androgen insensitivity syndrome) is the most common form of male pseudohermaphroditism, transmitted by means of maternal X-linked recessive gene. This syndrome is marked by unique combination; Normal female phenotype, normal male karyotype, 46,XY, normal or slightly elevated male blood testosterone levels and a high LH. Clinically, the diagnosis should be considered in a female with inguinal hernias, a patient with primary amenorrhea and absent uterus. we present a case testicular feminization syndrome with blindly ended vagina and inguinal masses with a brief review of literatures.
Keywords :Testicular feminization syndrome
