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Case Report
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Korean J Obstet Gynecol. 2012;55(10):756-760. Published online October 10, 2012.
DOI: https://doi.org/10.5468/KJOG.2012.55.10.756
- A case of juvenile xanthogranuloma involving skin and multiple systemic organs in a fetus.
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Eunjin Kim, Hye Young Kim, Jae Ho Lee, Chan Wook Park, Joong Shin Park, Jong Kwan Jun
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Department of Obstetrics and Gynecology, Seoul National University College of Medicine, Seoul, Korea. jsparkmd@snu.ac.kr
- Abstract
- Juvenile xanthogranuloma is a benign histiocytic proliferative disorder. It typically presents as a solitary, benign, rapidly growing cutaneous tumor that may regress spontaneously. Most of juvenile xanthogranuloma occur in infants and young children. We had experienced a case of juvenile xanthogranuloma in a fetus which involves multiple systemic organs. On prenatal ultrasonography, the fetus presented with pulmonary, perineal and hepatic nodules. The neonate was diagnosed with juvenile xanthogranuloma by the cutaneous and perineal nodule biopsy after birth. The neonate outpatient follow-up shows spontaneous regression without specific treatment. So we report a case with a brief review of the literature.
Keywords :Juvenile xanthogranuloma;Fetus;Systemic involvement;Multiple;Congenital
