A Case of Interrupted Aortic Arch Diagnosed by Fetal Echocardiography.

Kim, Sung Hoon; Park, Yong Won; Han, Sung Sik; Lee, Yeon Hye; Gwon, Hye Gyung; Lee, Chang Hee; Kim, Young Han; Lee, Gyung Joo

Case Report

Korean Journal of Obstetrics & Gynecology 2001;44(1):208-211.
Published online January 1, 2001.

A Case of Interrupted Aortic Arch Diagnosed by Fetal Echocardiography.

Sung Hoon Kim, Yong Won Park, Sung Sik Han, Yeon Hye Lee, Hye Gyung Gwon, Chang Hee Lee, Young Han Kim, Gyung Joo Lee

Department of Obstetrics and Gynecology, Yonsei University College of Medicine, Seoul, Korea.

Abstract

Interrupted aortic arch is a extreme type of coarctation of aorta and mostly associated with other cardiac anomalies. Unless there were no proper management, about 90% of babies would be dead in their neonatal period. A 28-year-old nulliparous woman was refered to our hospital for fetal echocardiography at 23 weeks' gestation with an abnormal prenatal ultrasonographic findings. We found interrupted aortic arch(type A), which was located in distal portion of the left subclavian artery, and ventricular septal defect. After 5 months follow up, the baby was vaginally delivered at 40 weeks' gestation. This baby was delivered at 40 weeks' gestation of a male infant with APGAR scores of 8 and 9 at 1 and 5 minutes, respectively. Neonatal echocardiography and electron beam tomography revealed interrupted aortic arch(type A), ventricular septal defect(subaortic type), patent ductus arteriosus, and atrial septal defect(ostium secondum defect). At the 10th day of birth, the infant was performed the operation of end to end anastomosis of desending aorta, patch repair of atrial septal defect, ligation of patent ductus arteriosus, and direct closure of patent foramen ovale.

Key Words: Interrupted aortic arch, Fetal Echocardiography